Case Report


DOI :10.17096/jiufd.70673   IUP :10.17096/jiufd.70673    Full Text (PDF)

Piknodizostozisli Üç Olgunun Klinik ve Sefalometrik Analizi: Olgu Sunumu

Eser ÇapanSerap TuranHülya Kılıçoğlu

Bu çalışma ender rastlanan piknodizostozisli üç olgunun ağız dışı ve içi bulguları ile sefalometrik değerlendirmesini sunmaktadır. Piknodizostozisli üç olgunun ağız dışı ve ağız içi bulguları klinik olarak değerlendirilmiş, hastalardan alınan lateral sefalometrik radyografiler üzerinde iskeletsel ve dişsel ölçümler gerçekleştirilmiştir. Olguların ikisinde maksiller retrognatiye bağlı iskeletsel sınıf III yapı, diğerinde ise bimaksiller retrüzyon ile beraber sınıf I yapı mevcuttur. Tüm hastalarda total sirküler çapraz kapanış, artmış gonial açı ve dik yön yüz boyutları, derin damak kubbesi ile üst dudakta retrüzyon gözlenmiştir. Bu tip olguların tedavisinde büyüme-gelişme dönemi de göz önünde bulundurularak maksiller genişletme, yüz maskesi veya ortognatik cerrahi tedavi alternatifleri arasındadır. Piknodizostozisli hastalarda kemik kırılganlığı ve diş çekimlerinden sonra osteomyelit riskinin yüksek olması nedeniyle yapılacak ortodontik tedavi ve ortognatik cerrahi müdahalelerde bu durum gözönüne alınarak hastaya yaklaşımda bulunulmalıdır.

DOI :10.17096/jiufd.70673   IUP :10.17096/jiufd.70673    Full Text (PDF)

CLINICAL AND CEPHALOMETRIC ANALYSIS OF THREE CASES WITH PYCNODYSOSTOSIS: CASE REPORTS

Eser ÇapanSerap TuranHülya Kılıçoğlu

The aim of this article is to present intra- and extra-oral and cephalometric findings of three patients with a rare disease: the pycnodysostosis. Two cases had skeletal Class III malocclusion due to maxillary retrognathia and one had bimaxillary retrusion with Class I relationship. Total circular crossbite, increased gonial angle and vertical facial proportions, deep-narrow palates and retruded upper lip were found in all cases. Maxillary expansion, face mask treatment or/and orthognathic surgery are treatment alternatives, considering the growth and development. Bone fragility and the risk of osteomyelitis after extractions should be considered in such cases before orthodontic treatment and orthognatic surgery.


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References

  • Maroteaux P, Lamy M. [Pyknodysostosis]. Presse Med 1962;70:999-1002. google scholar
  • Norholt SE, Bjerregaard J, Mosekilde L. Maxillary distraction osteogenesis in a patient with pycnodysostosis: a case report. J Oral Maxillofac Surg 2004;62(8):1037-1040. google scholar
  • Alves Pereira D, Berini Aytes L, Gay Escoda C. Pycnodysostosis. A report of 3 clinical cases. Med Oral Patol Oral Cir Bucal 2008;13(10):633-635. google scholar
  • Bathi RJ, Masur VN. Pyknodysostosis--a report of two cases with a brief review of the literature. Int J Oral Maxillofac Surg 2000;29(6):439-442. google scholar
  • O’Connell AC, Brennan MT, Francomano CA. Pycnodysostosis: orofacial manifestations in two pediatric patients. Pediatr Dent 1998;20(3):204-207. google scholar
  • Fonteles CS, Chaves CM Jr, Da Silveira A, Soares EC, Couto JL, de Azevedo Mde F. Cephalometric characteristics and dentofacial abnormalities of pycnodysostosis: report of four cases from Brazil. Oral Surg Oral Med Oral Pathol Oral Radiol Endod 2007;104(4):83-90. google scholar
  • Sedano H., Gorlin RJ, Andersen VE. Pycnodysostosis. Clinical and genetic consedirations Am J Dis Child 1968;116(1):70-77. google scholar
  • Hunt NP, Cunningham SJ, Adnan N, Harris M. The dental, craniofacial, and biochemical features of pyknodysostosis: a report of three new cases. J Oral Maxillofac Surg 1998;56(4):497-504. google scholar
  • Kamak H, Kamak G, Yavuz I. Clinical, radiographic, diagnostic and cephalometric features of pycnodysostosis in comparison with Turkish cephalometric norms: A case report Eur J Dent 2012;6(4):454-459. google scholar
  • Muto T, Yamazaki A, Takeda S, Tsuji Y, Shibata T. Pharyngeal narrowing as a common feature in pycnodysostosis--a cephalometric study. Int J Oral Maxillofac Surg 2005;34(6):680-685. google scholar
  • Ortegosa MV, Bertola DR, Aguena M, Passos-Bueno MR, Kim CA, de Faria ME. Challenges in the orthodontic treatment of a patient with pycnodysostosis. Cleft Palate Craniofac J 2013;51(6):735-739. google scholar
  • Hernandez-Alfaro F, Arenaz Bua J, Serra Serrat M, Mareque Bueno J. Orthognathic surgery in pycnodysostosis: a case report. Int J Oral Maxillofac Surg 2011;40(1):110-113. google scholar
  • Raposo-Amaral CE, Tong A, Denadai R, Yalom A, Raposo-Amaral CA, Bertola D, Li A, Jarrahy R. A subcranial Le Fort III advancement with distraction osteogenesis as a clinical strategy to approach pycnodysostosis with midface retrusion and exorbitism. J Craniofac Surg 2013;24(4):1327-1330. google scholar
  • Varol A, Sabuncuoglu FA, Sencimen M, Akcam T, Olmez H, Basa S. Rigid external maxillary distraction and rhinoplasty for pyknodysostosis. J Craniofac Surg 2011;22(3):901-904. google scholar

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APA

Çapan, E., Turan, S., & Kılıçoğlu, H. (2015). Piknodizostozisli Üç Olgunun Klinik ve Sefalometrik Analizi: Olgu Sunumu. European Oral Research, 49(1), 51-55. https://doi.org/10.17096/jiufd.70673


AMA

Çapan E, Turan S, Kılıçoğlu H. Piknodizostozisli Üç Olgunun Klinik ve Sefalometrik Analizi: Olgu Sunumu. European Oral Research. 2015;49(1):51-55. https://doi.org/10.17096/jiufd.70673


ABNT

Çapan, E.; Turan, S.; Kılıçoğlu, H. Piknodizostozisli Üç Olgunun Klinik ve Sefalometrik Analizi: Olgu Sunumu. European Oral Research, [Publisher Location], v. 49, n. 1, p. 51-55, 2015.


Chicago: Author-Date Style

Çapan, Eser, and Serap Turan and Hülya Kılıçoğlu. 2015. “Piknodizostozisli Üç Olgunun Klinik ve Sefalometrik Analizi: Olgu Sunumu.” European Oral Research 49, no. 1: 51-55. https://doi.org/10.17096/jiufd.70673


Chicago: Humanities Style

Çapan, Eser, and Serap Turan and Hülya Kılıçoğlu. Piknodizostozisli Üç Olgunun Klinik ve Sefalometrik Analizi: Olgu Sunumu.” European Oral Research 49, no. 1 (Jun. 2025): 51-55. https://doi.org/10.17096/jiufd.70673


Harvard: Australian Style

Çapan, E & Turan, S & Kılıçoğlu, H 2015, 'Piknodizostozisli Üç Olgunun Klinik ve Sefalometrik Analizi: Olgu Sunumu', European Oral Research, vol. 49, no. 1, pp. 51-55, viewed 6 Jun. 2025, https://doi.org/10.17096/jiufd.70673


Harvard: Author-Date Style

Çapan, E. and Turan, S. and Kılıçoğlu, H. (2015) ‘Piknodizostozisli Üç Olgunun Klinik ve Sefalometrik Analizi: Olgu Sunumu’, European Oral Research, 49(1), pp. 51-55. https://doi.org/10.17096/jiufd.70673 (6 Jun. 2025).


MLA

Çapan, Eser, and Serap Turan and Hülya Kılıçoğlu. Piknodizostozisli Üç Olgunun Klinik ve Sefalometrik Analizi: Olgu Sunumu.” European Oral Research, vol. 49, no. 1, 2015, pp. 51-55. [Database Container], https://doi.org/10.17096/jiufd.70673


Vancouver

Çapan E, Turan S, Kılıçoğlu H. Piknodizostozisli Üç Olgunun Klinik ve Sefalometrik Analizi: Olgu Sunumu. European Oral Research [Internet]. 6 Jun. 2025 [cited 6 Jun. 2025];49(1):51-55. Available from: https://doi.org/10.17096/jiufd.70673 doi: 10.17096/jiufd.70673


ISNAD

Çapan, Eser - Turan, Serap - Kılıçoğlu, Hülya. Piknodizostozisli Üç Olgunun Klinik ve Sefalometrik Analizi: Olgu Sunumu”. European Oral Research 49/1 (Jun. 2025): 51-55. https://doi.org/10.17096/jiufd.70673



TIMELINE


Submitted06.04.2014
Accepted19.06.2014
Published Online25.03.2015

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