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Case Report


DOI :10.17096/jiufd.72612   IUP :10.17096/jiufd.72612    Full Text (PDF)

CLINICAL AND RADIOGRAPHIC FEATURES OF PARRY-ROMBERG SYNDROME

Mithula Naır, Vidya Ajıla, Shruthi Hegde, G. Subhas Babu, Rumela Ghosh

Parry-Romberg syndrome or progressive hemifacial atrophy is a craniofacial disorder characterized by slow and progressive atrophy, generally unilateral, of facial tissues including muscles, bones and skin. The coup de sabre is a clear line of demarcation seen between the normal and abnormal structures. The severity of the facial deformity is dependent on the age of onset of the disease. Cosmetic management is the only available treatment and has to be delayed until facial growth is completed. The present case report deals with a 43-year-old woman with progressive hemifacial atrophy which started from the age of 10 months. Despite almost complete involvement of the right paramedian area and the early age of onset, she had neither eye changes nor any dental malformations.

Keywords: Parry-Romberg syndrome, progressive atrophy, hemifacial, craniofacial disorder, treatment
DOI :10.17096/jiufd.72612   IUP :10.17096/jiufd.72612    Full Text (PDF)

PARRY-ROMBERG SENDROMUNUN KLİNİK VE RADYOGRAFİK ÖZELLİKLERİ

Mithula Naır, Vidya Ajıla, Shruthi Hegde, G. Subhas Babu, Rumela Ghosh

Parry-Romberg sendromu ya da progresif hemifasiyal atrofi; yüz bölgesinde kas, kemik ve cilt dokusunda genellikle tek taraflı olarak görülen, yavaş ve progresif atrofi ile karakterize bir klinik tablodur. Normal ve anormal dokular arasındaki belirgin çizgiye kılıç darbesine benzetilerek “coup de sabre” adı verilmiştir. Yüz deformitesinin ciddiyeti hastalığın ortaya çıktığı yaşa göre değişir. Bu hastalarda kozmetik tedavi başlıca seçenek olmasına karşılık yüz gelişimi tamamlanıncaya kadar ertelenmelidir. Bu olgu bildirisinde 10 aylıkken progresif hemifasiyal atrofi teşhisi koyulan 43 yaşındaki bir kadın hasta sunulmuştur. Sendromun erken yaşta başlamasına ve neredeyse yüzün sağ yarısının tamamını etkilemesine rağmen hastada gözlerle ilgili bir bulguya ya da dişlerle ilgili bir gelişim bozukluğuna rastlanmamıştır

Keywords: Parry-Romberg sendromu, progresif atrofi, hemifasiyal, kraniofasiyal bozukluk, tedavi

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References

  • 1. Ayyildiz O, Ayyildiz S, Durukan AH, Sobaci G. Progressive hemifacial atrophy with contralateral uveitis: A case report. Iran Red Crescent Med J 2015;17(9):e16168. google scholar
  • 2. Balan P, Gogineni SB, Shetty SR, D’Souza D. Three-dimensional imaging of progressive facial hemiatrophy (parry-romberg syndrome) with unusual conjunctival findings. Imaging Sci Dent 2011;41(4):183-187. google scholar
  • 3. Kaya M, Sel Yilmaz C, Kurtaran H, Gunduz M. Chronologic presentation of a severe case of progressive hemifacial atrophy (parry-romberg syndrome) with the loss of an eye. Case Rep Otolaryngol 2014;2014:703017. google scholar
  • 4. Sudarshan R. Progressive hemi facial atrophy- a review. SEAJCRR 2012;1(1):16-21. google scholar
  • 5. Deshingkar SA, Barpande SR, Bhavthankar JD, Humbe JG. Progressive hemifacial atrophy (parry-romberg syndrome). Contemp Clin Dent 2012;3(Suppl 1):S78-81. google scholar
  • 6. Khan M, Khan M, Negi R, Gupta N. Parry romberg syndrome with localized scleroderma: A case report. J Clin Exp Dent 2014;6(3):e313-316. google scholar
  • 7. Grippaudo C, Deli R, Grippaudo FR, Di Cuia T, Paradisi M. Management of craniofacial development in the parry-romberg syndrome: Report of two patients. Cleft Palate Craniofac J 2004;41(1):95-104. google scholar
  • 8. Pinheiro TP, Silva CC, Silveira CS, Botelho PC, Pinheiro M, Pinheiro Jde J. Progressive hemifacial atrophy--case report. Med Oral Patol Oral Cir Bucal 2006;11(2):E112-114. google scholar
  • 9. Erfan M, Khan I, Ahmed AS, Hasnain S. A tale of two diseases: Parry romberg syndrome and en coup de sabre: A case report. Int J Pathol 2015;13(2):82-86. google scholar
  • 10. Kumar AA, Kumar RA, Shantha GP, Aloogopinathan G. Progressive hemi facial atrophy - parry romberg syndrome presenting as severe facial pain in a young man: A case report. Cases J 2009;2:6776. google scholar
  • 11. Gomez-Diez SG, Lopez LG, Escobar ML, Gutierrez LJ, Oliva NP. Progressive facial hemiatrophy with associated osseous lesions. Med Oral Patol Oral Cir Bucal 2007;12(8):E602-604. google scholar

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APA

Naır, M., Ajıla, V., Hegde, S., Babu, G.S., & Ghosh, R. (2017). CLINICAL AND RADIOGRAPHIC FEATURES OF PARRY-ROMBERG SYNDROME. European Oral Research, 51(3), 45-49. https://doi.org/10.17096/jiufd.72612


AMA

Naır M, Ajıla V, Hegde S, Babu G S, Ghosh R. CLINICAL AND RADIOGRAPHIC FEATURES OF PARRY-ROMBERG SYNDROME. European Oral Research. 2017;51(3):45-49. https://doi.org/10.17096/jiufd.72612


ABNT

Naır, M.; Ajıla, V.; Hegde, S.; Babu, G.S.; Ghosh, R. CLINICAL AND RADIOGRAPHIC FEATURES OF PARRY-ROMBERG SYNDROME. European Oral Research, [Publisher Location], v. 51, n. 3, p. 45-49, 2017.


Chicago: Author-Date Style

Naır, Mithula, and Vidya Ajıla and Shruthi Hegde and G. Subhas Babu and Rumela Ghosh. 2017. “CLINICAL AND RADIOGRAPHIC FEATURES OF PARRY-ROMBERG SYNDROME.” European Oral Research 51, no. 3: 45-49. https://doi.org/10.17096/jiufd.72612


Chicago: Humanities Style

Naır, Mithula, and Vidya Ajıla and Shruthi Hegde and G. Subhas Babu and Rumela Ghosh. “CLINICAL AND RADIOGRAPHIC FEATURES OF PARRY-ROMBERG SYNDROME.” European Oral Research 51, no. 3 (Apr. 2025): 45-49. https://doi.org/10.17096/jiufd.72612


Harvard: Australian Style

Naır, M & Ajıla, V & Hegde, S & Babu, GS & Ghosh, R 2017, 'CLINICAL AND RADIOGRAPHIC FEATURES OF PARRY-ROMBERG SYNDROME', European Oral Research, vol. 51, no. 3, pp. 45-49, viewed 2 Apr. 2025, https://doi.org/10.17096/jiufd.72612


Harvard: Author-Date Style

Naır, M. and Ajıla, V. and Hegde, S. and Babu, G.S. and Ghosh, R. (2017) ‘CLINICAL AND RADIOGRAPHIC FEATURES OF PARRY-ROMBERG SYNDROME’, European Oral Research, 51(3), pp. 45-49. https://doi.org/10.17096/jiufd.72612 (2 Apr. 2025).


MLA

Naır, Mithula, and Vidya Ajıla and Shruthi Hegde and G. Subhas Babu and Rumela Ghosh. “CLINICAL AND RADIOGRAPHIC FEATURES OF PARRY-ROMBERG SYNDROME.” European Oral Research, vol. 51, no. 3, 2017, pp. 45-49. [Database Container], https://doi.org/10.17096/jiufd.72612


Vancouver

Naır M, Ajıla V, Hegde S, Babu GS, Ghosh R. CLINICAL AND RADIOGRAPHIC FEATURES OF PARRY-ROMBERG SYNDROME. European Oral Research [Internet]. 2 Apr. 2025 [cited 2 Apr. 2025];51(3):45-49. Available from: https://doi.org/10.17096/jiufd.72612 doi: 10.17096/jiufd.72612


ISNAD

Naır, Mithula - Ajıla, Vidya - Hegde, Shruthi - Babu, G.Subhas - Ghosh, Rumela. “CLINICAL AND RADIOGRAPHIC FEATURES OF PARRY-ROMBERG SYNDROME”. European Oral Research 51/3 (Apr. 2025): 45-49. https://doi.org/10.17096/jiufd.72612



TIMELINE


Submitted23.01.2017
Accepted15.02.2017

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