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Case Study


DOI :10.17096/jiufd.96279   IUP :10.17096/jiufd.96279    Full Text (PDF)

MELKERSSON-ROSENTHAL SYNDROME: A CASE REPORT

Adil Başman, Mustafa Gümüşok, Şerife Değerli, Mustafa Kaya, Meryem Toraman alkurt

Melkersson-Rosenthal Syndrome (MRS) is a rare disorder consisting of a triad of persistent or recurrent orofacial edema, relapsing facial paralysis and fissured tongue. It is rarely possible to observe all aspects of the classical triad at the same time, since these symptoms may appear in different times of life cycle. The most common symptom is orofacial edema. Although etiology of MRS is unclear, various factors such as infections, genetic predisposition, immune deficiency, food intolerance and stress have been held responsible. MRS is diagnosed based on clinical features. This case report describes a 39 years old male patient with recurrent swelling of the upper lip. Clinical examinations showed classical triad of MRS. The diagnosis and treatment procedures were presented with special emphasis to the clinical features of this rare condition.
Keywords: Melkersson-Rosenthal Syndrome, orofacial edema, fissured tongue, steroid use
DOI :10.17096/jiufd.96279   IUP :10.17096/jiufd.96279    Full Text (PDF)

Melkersson-Rosenthal Sendromu: Olgu Sunumu

Adil Başman, Mustafa Gümüşok, Şerife Değerli, Mustafa Kaya, Meryem Toraman alkurt

Melkersson-Rosenthal Sendromu (MRS), tekrarlayan periferik fasiyal paralizi, tekrarlayan ya da kalıcı fasiyal ödem ve fissürlü dil triadı ile karakterize nadir görülen bir hastalıktır. Etyolojisi tam olarak bilinmemekle birlikte, enfeksiyonlar, genetik yatkınlık, immün yetmezlik, besin intoleransı ve stres faktörleri gibi faktörlerin etkili olabileceği düşünülmektedir. Klasik triad her zaman birlikte bulunmayabilir, bulgular farklı zamanlarda tek tek de ortaya çıkabilir. En sık görülen bulgu orofasiyal ödemdir. MRS tanısı klinik bulgularla konulur. Bu olgu bildirisinde, üst dudağında tekrarlayan, şişlik ile şikayeti ile kliniğimize başvuran, MRS’nin klasik tiradına sahip 39 yaşındaki erkek hastanın klinik bulguları ile birlikte teşhis ve tedavisi sunulmuştur.
Keywords: Melkersson-Rosenthal Sendromu, Orofasiyal ödem, fissürlü dil, steroid kullanımı

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APA

Başman, A., Gümüşok, M., Değerli, Ş., Kaya, M., & Toraman alkurt, M. (2017). MELKERSSON-ROSENTHAL SYNDROME: A CASE REPORT. European Oral Research, 51(1), 42-45. https://doi.org/10.17096/jiufd.96279


AMA

Başman A, Gümüşok M, Değerli Ş, Kaya M, Toraman alkurt M. MELKERSSON-ROSENTHAL SYNDROME: A CASE REPORT. European Oral Research. 2017;51(1):42-45. https://doi.org/10.17096/jiufd.96279


ABNT

Başman, A.; Gümüşok, M.; Değerli, Ş.; Kaya, M.; Toraman alkurt, M. MELKERSSON-ROSENTHAL SYNDROME: A CASE REPORT. European Oral Research, [Publisher Location], v. 51, n. 1, p. 42-45, 2017.


Chicago: Author-Date Style

Başman, Adil, and Mustafa Gümüşok and Şerife Değerli and Mustafa Kaya and Meryem Toraman alkurt. 2017. “MELKERSSON-ROSENTHAL SYNDROME: A CASE REPORT.” European Oral Research 51, no. 1: 42-45. https://doi.org/10.17096/jiufd.96279


Chicago: Humanities Style

Başman, Adil, and Mustafa Gümüşok and Şerife Değerli and Mustafa Kaya and Meryem Toraman alkurt. “MELKERSSON-ROSENTHAL SYNDROME: A CASE REPORT.” European Oral Research 51, no. 1 (Jun. 2024): 42-45. https://doi.org/10.17096/jiufd.96279


Harvard: Australian Style

Başman, A & Gümüşok, M & Değerli, Ş & Kaya, M & Toraman alkurt, M 2017, 'MELKERSSON-ROSENTHAL SYNDROME: A CASE REPORT', European Oral Research, vol. 51, no. 1, pp. 42-45, viewed 29 Jun. 2024, https://doi.org/10.17096/jiufd.96279


Harvard: Author-Date Style

Başman, A. and Gümüşok, M. and Değerli, Ş. and Kaya, M. and Toraman alkurt, M. (2017) ‘MELKERSSON-ROSENTHAL SYNDROME: A CASE REPORT’, European Oral Research, 51(1), pp. 42-45. https://doi.org/10.17096/jiufd.96279 (29 Jun. 2024).


MLA

Başman, Adil, and Mustafa Gümüşok and Şerife Değerli and Mustafa Kaya and Meryem Toraman alkurt. “MELKERSSON-ROSENTHAL SYNDROME: A CASE REPORT.” European Oral Research, vol. 51, no. 1, 2017, pp. 42-45. [Database Container], https://doi.org/10.17096/jiufd.96279


Vancouver

Başman A, Gümüşok M, Değerli Ş, Kaya M, Toraman alkurt M. MELKERSSON-ROSENTHAL SYNDROME: A CASE REPORT. European Oral Research [Internet]. 29 Jun. 2024 [cited 29 Jun. 2024];51(1):42-45. Available from: https://doi.org/10.17096/jiufd.96279 doi: 10.17096/jiufd.96279


ISNAD

Başman, Adil - Gümüşok, Mustafa - Değerli, Şerife - Kaya, Mustafa - Toraman alkurt, Meryem. “MELKERSSON-ROSENTHAL SYNDROME: A CASE REPORT”. European Oral Research 51/1 (Jun. 2024): 42-45. https://doi.org/10.17096/jiufd.96279



TIMELINE


Accepted10.03.2016
Published Online02.01.2017

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